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60 2021

Journal of Food and Nutrition Research
Súhrny čísla 2 / 2021

Scortegagna, M. L. – Oliveira, V. R. – Lobato, C. M. D. – Doneda, D.
Evaluation and acceptability of alternative food recipes for patients with phenylketonuria
Journal of Food and Nutrition Research, 60, 2021, č. 2, s. 131-137

Viviani Ruffo de Oliveira, Nutrition Department, Postgraduate Program in Food, Nutrition and Health, Federal University of Rio Grande do Sul, Rua Ramiro Barcellos 2400, 90035-002 Porto Alegre, Brazil. E-mail:

Received 7 July 2020; 1st revised 9 March 2021; 2nd revised 29 March 2021; accepted 14 April 2021; published online 1 June 2021.

Súhrn: Phenylketonuria (PKU) is an inborn error of metabolism, treatment of which is based on phenylalanine restriction diet. This study aimed to identify studies with developed recipes and food products as well as sensory analysis for patients with PKU. The search was performed in Coordination Agency for Advanced Training of Graduate Personnel (Capes – Brasília, Distrito Federal, Brazil), National Library of Medicine (PubMed – National Institutes of Health, Bethesda, Maryland, USA), Latin American and Caribbean Health Science Literature (Lilacs – Sao Paulo, Brazil) and Cochrane Library (Cohcrane – London, United Kingdom). Articles were selected in these databases without date restrictions. After the filter addition and through the selected articles’ list of references, 12 articles were included in this study with recipes and food for patients with PKU (bakery products, dairy beverages and juices). The results suggest that the production of PKU foods was feasible and could be made at home, since these food preparations were easy and contained low-cost ingredients. Results also suggest that more food surveys are carried out in periphery countries, where special products are difficult to find and expensive to purchase, besides improving viable food preparations in the family environment.

Kľúčové slová: phenylketonuria; phenylalanine restriction; phenylketonuria recipes; sensory evaluation

Na stiahnutie:
  jfnr202111-2021-2-pp131-137-scortegagna.pdf (PDF, 366.8 Kb, 422x)